PHARYNGEAL-CERVICAL-BRACHIAL VARIANT: AN UNUSUAL PRESENTATION OF GUILLAIN-BARRÉ SYNDROME

Main Article Content

Muhammad Furrukh
Saeed Bin Ayaz
http://orcid.org/0000-0002-4894-9325
Fatima Ayaz

Abstract

Pharyngeal-cervical-brachial (PCB) variant is a rare presentation of Guillain–Barré syndrome (GBS), which is symbolized by oroparhyngeal, cervical and upper limb weakness. It is often wrongly diagnosed as brainstem stroke, myasthenia gravis or botulism. The presence of anti-GT1a and anti-GQ1b ganglioside IgG antibodies and axonal electrophysiological pattern are the hallmark of PCB variant. The treatment is similar to any other variant of GBS. We present here, report of a 20-year-old male, who presented with findings suggestive of PCB variant of GBS but had absent anti-GT1a and anti-GQ1b antibodies and a normal cerebrospinal fluid. He made a remarkable recovery after administration of intravenous immunoglobulins.

Article Details

How to Cite
Furrukh, M., S. Ayaz, and F. Ayaz. “PHARYNGEAL-CERVICAL-BRACHIAL VARIANT: AN UNUSUAL PRESENTATION OF GUILLAIN-BARRÉ SYNDROME”. KHYBER MEDICAL UNIVERSITY JOURNAL, Vol. 11, no. 1, Mar. 2019, pp. 45-47, doi:10.35845/kmuj.2019.18271.
Section
Case Report
Author Biographies

Muhammad Furrukh, Holy Family Hospital, Rawalpindi, Pakistan

Registrar Internal Medicine

Saeed Bin Ayaz, Combined Military Hospital Quetta and Quetta Institute of Medical Sciences, Quetta

Department of Rehabilitation Medicine

Fatima Ayaz, Holy Family Hospital, Rawalpindi, Pakistan.

Registrar Internal Medicine

References

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